1 Jul 2007Case Report
Ovarian cyst in a case of female pseudohermaphroditism in a patient with male phenotype
Mario Benedetti 1Francesco Tinozzi 1Simone Albertario 1Carlo Bianchi 1Luigi Valenti 1Tekla Niebel 1Stefano Tinozzi 1Stefano Dini 1Nirvana Moroni 1
Affiliations
Article Info
1 Università degli Studi di Pavia, Istituto di Chirurgia Generale e dei Trapianti d’Organo, Chirurgia Gastroenterologica e Mammaria, IRCCS Policlinico “S. Matteo”, Pavia
Ann. Ital. Chir., 2007, 78(4), 329-332;
Published: 1 Jul 2007
Copyright © 2007 Annali Italiani di Chirurgia
This work is licensed under a Creative Commons Attribution 4.0 International License.
Abstract
Female pseudohermaphroditism is an intersexual state distinguished by virilized external genitals and secondary sex characters in a XX subject. We report a case of female pseudohermaphroditism diagnosed later on the discovery of an abdominal mass, then revealed to be an enormous ovarian cyst. Hormonal dosages suggested the presence of partial surrenalic b-hydroxylase deficiency. For this reason the clinical picture was considered expression of an adreno-genital syndrome, displayed as female pseudohermaphroditism with Prader stage V virilization.
Keywords
- Abdominal mass
- Female pseudohermaphroditism
- Ovarian cist
