A case of Poland’s syndrome in a 2-year-old female is described. The patient had come to our Emergency department for abdominal pain. The thorax’s asymmetric depression and the brachysyndactyly of the right hand are fundamental elements to make Poland’s syndrome diagnosis in our patient. In this report, the different formes of Poland’s syndrome, the classification and the indications for a surgical intervention are described. Besides the importance of a precocious diagnosis is underlined, due to avoid complications related to late rehabilitation and multidisciplinary approach to the patient.